Definition

Gastroschisis repair is a procedure done on an infant to correct a birth defect that causes an opening in the skin and muscles covering the belly (abdominal wall). The opening allows the intestines and sometimes other organs to bulge outside the belly.

Alternative Names

Abdominal wall defect repair - gastroschisis

Description

The goal of the procedure is to place the organs back into the baby's belly and fix the defect. Repair may be done right after the baby is born. This is called a primary repair. Or, the repair is done in stages. This is called a staged repair. Surgery for primary repair is done in the following way:

• If possible, the surgery is performed the day your baby is born. This surgery is done when there is only a small amount of intestine outside the belly and the intestine isn't very swollen.
• Right after birth, the intestine that is outside the belly is placed in a special bag or is covered with a plastic wrap to protect it.
• Your baby is then prepared for surgery.
• Your baby receives general anesthesia. This is medicine that allows your baby to sleep and be pain-free during the operation.
• The surgeon examines your baby's intestine (bowel) closely for signs of damage or other birth defects. Unhealthy parts are removed. The healthy edges are stitched together.
• The intestine is placed back into the belly.
• The opening in the wall of the belly is repaired.

Staged repair is done when your baby isn't stable enough for primary repair. It may also be done if the baby's intestine is very swollen or there is a large amount of intestine outside the body. Or, it is done when the baby's belly isn't large enough to contain all of the intestine. The repair is performed the following way:

• Right after birth, the baby's intestine and any other organs that are outside the belly are placed in a long plastic pouch. This pouch is called a silo. The silo is then attached to the baby's belly.
• The other end of the silo is hung above the baby. This allows gravity to help the intestine to slip into the belly. Each day, the health care provider also gently tightens the silo to push the intestine into the belly.
• It may take up to 2 weeks for all of the intestine and any other organs to be back inside the belly. The silo is then removed. The opening in the belly is repaired.

More surgery may be needed at a later time to repair the muscles in your baby's belly.

Why the Procedure Is Performed

Gastroschisis is a life-threatening condition. It needs to be treated soon after birth so that the baby's organs can develop and be protected in the belly.

Risks

Risks for anesthesia and surgery in general are:

• Allergic reactions to medicines
• Breathing problems
• Bleeding
• Infection

Risks for gastroschisis repair are:

• Breathing problems if the baby's belly area (abdominal space) is smaller than normal. The baby may need a breathing tube and breathing machine for a few days or weeks after surgery.
• Inflammation of tissues that line the wall of the abdomen and cover the abdominal organs.
• Organ injury.
• Problems with digestion and absorbing nutrients from food, if a baby has a lot of damage to the small bowel.
• Temporary paralysis (intestinal muscles stop moving) of the small bowel.
• Abdominal wall hernia.

Before the Procedure

Gastroschisis is usually seen on ultrasound before the baby is born. The ultrasound may show loops of bowel freely floating outside the baby's belly.

After gastroschisis is found, your baby will be followed very closely to make sure they are growing.

Your baby should be delivered at a hospital that has a neonatal intensive care unit (NICU) and a pediatric surgeon. A NICU is set up to handle emergencies that occur at birth. A pediatric surgeon has special training in surgery for babies and children. Most babies who are known to have gastroschisis are delivered by cesarean section (C-section).

After the Procedure

After surgery, your baby will receive care in the NICU. Your baby will be placed in a special bed to keep warm.

Your baby may need to be on a breathing machine until organ swelling has decreased and the size of the belly area has increased.

Other treatments your baby will probably need after surgery are:

• A nasogastric (NG) tube placed through the nose to drain the stomach and keep it empty.
• Antibiotics.
• Fluids and nutrients given through a vein.
• Oxygen.
• Pain medicines.

Feedings are started through the NG tube as soon as your baby's bowel starts functioning after surgery. Feedings by mouth will start very slowly. Your baby may eat slowly and may need feeding therapy, lots of encouragement, and time to recover after a feeding.

The average stay in the hospital is a few weeks up to a few months. You may be able to take your baby home once they start taking all foods by mouth and gaining weight.

Outlook (Prognosis)

After you go home, your child may develop a blockage in the intestines (bowel obstruction) due to a kink or scar in the intestines. The health care provider can tell you how this will be treated.

Most of the time, gastroschisis can be corrected with one or two surgeries. How well your baby does will depend on how much damage there was to the intestine.

After recovering from surgery, most children with gastroschisis do very well and live normal lives. Most babies who are born with gastroschisis do not have any other birth defects.

References

Chung DH. Pediatric surgery. In: Townsend CM Jr, Beauchamp RD, Evers BM, Mattox KL, eds. Sabiston Textbook of Surgery. 21st ed. Philadelphia, PA: Elsevier; 2022:chap 67.

Islam S. Congenital abdominal wall defects: gastroschisis and omphalocele. In: Holcomb GW, Murphy JP, St. Peter SD, eds. Holcomb and Ashcraft's Pediatric Surgery. 7th ed. Philadelphia, PA: Elsevier; 2020:chap 48.

Ledbetter DJ, Chabra S, Javid PJ. Abdominal wall defects. In: Gleason CA, Juul SE, eds. Avery's Diseases of the Newborn. 10th ed. Philadelphia, PA: Elsevier; 2018:chap 73.